Development of the Dentition in Cleidocranial Dysplasia

Resident: Roberts
Article title: Development of the Dentition in Cleidocranial Dysplasia
Author: Jensen, Birgit et al.
Journal: Oral Pathology Med
Year: 1990
Volume: 19 pages: 89-93
Discussion
The purpose of the article was to investigate dental anomalies involving 19 patients with Cleidocranial Dysplasia (CCD). The dentition was evaluated for formation, maturation and eruption of the dentition. The results indicated that formation of primary teeth was normal, wheras all patients but one had supernumerary permanent teeth. Frequency of supernumerary teeth ranged from 22% in the maxillary incisor region to 5% in the molar regions. Supernumerary teeth were formed lingually to the normal teeth. Maturation of the primary teeth was normal, while permanent teeth were delayed from 1 to 4 years. Supernumerary teeth were delayed about 4 years in relation to normal permanent teeth. Eruption of primary teeth was normal, wheras all patients had sever eruption problems of permanent teeth. It was hypothesized that the dental lamina for both primary and permanent dentition is normal, but does not resolve completely resulting in supernumerary teeth. Abnormalities of tooth morphology is related to inadequate space and arrested eruption. Delayed or arrested eruption is probably caused by diminished resorption of bone and of primary teeth and to the presence of multiple supernumerary teeth.
Assessment of article: The author did a great job of keeping things relevant to the clinician in this article.